Abstract: The auditory brainstem implants are designed for use in adults with Neurofibromatosis II in order to restore the hearing and assist them in being able to hear all the sounds in the environment. Recently, the ABI has also been indicated for use in children with congenital inner ear malformations who would not benefit from hearing aids or cochlear implantation is not feasible due to anomalous cochlea. The ABI’s have been recognized as an effective treatment option in children to reinstate the hearing.