Abstract: Anomalies in tooth development are variations in the number, shape, size and structure of dental structures. First clinical case: A 6-year-old girl attends the Department of Pediatric Dental Medicine at the Faculty of Dental Medicine, Medical University of Varna for prophylactic examination. Intraoral examination revealed the presence of an unilaterally unusually large tooth in the region of the upper left central primary incisor of the upper jaw.