Abstract: Extranodal natural killer/T cell lymphoma, nasal type, is a Non-Hodgkins lymphoma, most commonly affecting the nasal cavity, paranasal sinuses and nasopharynx. Clinically it is characterised by destruction of facial tissues, commencing in the midline. In most cases it either arises from malignant transformation of natural killer cells (NK) or cytotoxic T cells. Extranodal NK/T cell lymphoma, nasal type, is rare, but even rarer in females. The purpose of this article is to report a severe case of extranodal NK/T cell lymphoma, nasal type, in young south Indian female and improvement of midfacial swelling after radiotherapy.